Von Hippel-Lindau syndrome (VHLS) is a rare. autosomal dominant genetic disease with high penetrance and variable phenotypic expression caused by variants in the VHL gene. VHLS is associated with the presence of vascular tumors. often hemangioblastoma of the central nervous system. https://www.lecoureures.shop/product-category/ski-de-fond-equipement-batons/